ICD-11 classes
20 Developmental anomalies
Multiple developmental anomalies or syndromes

ICD-11 Multiple developmental anomalies or syndromes

Complex developmental anomalies involving more than one body system

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 20 clarifying diagnoses:

  1. LD20 — Syndromes with central nervous system anomalies as a major feature
    It contains 7 clarifying diagnoses.
  2. LD21 — Syndromes with eye anomalies as a major feature
    It contains 3 clarifying diagnoses.
  3. LD22 — Syndromes with dental anomalies as a major feature
    It contains 3 clarifying diagnoses.
  4. LD23 — Syndromes with vascular anomalies as a major feature
    It contains 2 clarifying diagnoses.
  5. LD24 — Syndromes with skeletal anomalies as a major feature
    It contains 24 clarifying diagnoses.
  6. LD25 — Syndromes with face or limb anomalies as a major feature
    It contains 6 clarifying diagnoses.
  7. LD26 — Syndromes with limb anomalies as a major feature
    It contains 9 clarifying diagnoses.
  8. LD27 — Syndromes with skin or mucosal anomalies as a major feature
    It contains 12 clarifying diagnoses.
  9. LD28 — Syndromes with connective tissue involvement as a major feature
    It contains 5 clarifying diagnoses.
  10. LD29 — Syndromes with obesity as a major feature
    It contains 1 clarifying diagnosis.
  11. LD2A — Malformative disorders of sex development
    It contains 10 clarifying diagnoses.
  12. LD2B — Syndromes with premature ageing appearance as a major feature
  13. LD2C — Overgrowth syndromes
  14. LD2D — Phakomatoses or hamartoneoplastic syndromes
    It contains 7 clarifying diagnoses.
  15. LD2E — Syndromes with structural anomalies due to inborn errors of metabolism
    It contains 7 clarifying diagnoses.
  16. LD2F — Syndromes with multiple structural anomalies, without predominant body system involvement
    It contains 14 clarifying diagnoses.
  17. LD2G — Conjoined twins
  18. LD2H — Syndromic genetic deafness
    It contains 10 clarifying diagnoses.
  19. LD2Y — Other specified multiple developmental anomalies or syndromes
  20. LD2Z — Multiple developmental anomalies or syndromes, unspecified

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