ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders

ICD-11 Metabolic disorders

The diagnosis has no description.

The diagnosis includes nothing.

It excludes 6 items.

  • androgen resistance syndrome (LD2A.4)
  • Congenital adrenal hyperplasia (5A71.01)
  • Ehlers-Danlos syndrome (LD28.1)
  • Hereditary haemolytic anaemia due to enzyme deficiency (3A10)
  • Marfan syndrome (LD28.01)
  • 5-alpha-reductase deficiency (5A81.1)

Diagnosis contains 9 clarifying diagnoses:

  1. Inborn errors of metabolism
    It contains 13 clarifying diagnoses.
  2. Disorders of metabolite absorption or transport
    It contains 7 clarifying diagnoses.
  3. Disorders of fluid, electrolyte or acid-base balance
    It contains 11 clarifying diagnoses.
  4. Disorders of lipoprotein metabolism or certain specified lipidaemias
    It contains 4 clarifying diagnoses.
  5. 5C90 — Metabolic or transporter liver disease
    It contains 16 clarifying diagnoses.
  6. Other metabolic disorders
    It contains 4 clarifying diagnoses.
  7. CA25 — Cystic fibrosis
    It contains 4 clarifying diagnoses.
  8. JA05.5 — Metabolic disorders following abortion, ectopic or molar pregnancy
  9. 5D2Z — Metabolic disorders, unspecified

The diagnosis is included in 2 other classes.

  • Cystic fibrosis (CA25)
  • Metabolic disorders following abortion, ectopic or molar pregnancy (JA05.5)

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