ICD-11 classes
08 Diseases of the nervous system
Disorders of autonomic nervous system

ICD-11 Disorders of autonomic nervous system

This is a group of conditions characterised as being in or associated with the autonomic nervous system, the component of the peripheral nervous system that regulates involuntary physiologic processes.

It includes 1 item.

  • Disorder of parasympathetic nervous system

The diagnosis excludes nothing.

Diagnosis contains 18 clarifying diagnoses:

  1. 8D80 — Congenital malformations of the autonomic nervous system
  2. 8D81 — Inherited autonomic nervous system disorders
  3. 8D82 — Autoimmune disorders involving the autonomic nervous system
  4. 8D83 — Autonomic nervous system disorder due to infection
  5. 8D84 — Pure autonomic nervous system failure
  6. 8D85 — Autonomic nervous system disorder due to substances
  7. 8D86 — Autonomic nervous system hyperactivity
  8. 8D87 — Autonomic nervous system disorder due to certain specified neurodegenerative disorder
    It contains 2 clarifying diagnoses.
  9. 8D88 — Autonomic neuropathies
    It contains 8 clarifying diagnoses.
  10. 8D89 — Disorders of orthostatic tolerance
    It contains 7 clarifying diagnoses.
  11. 8D8A — Focal or segmental autonomic disorders
    It contains 7 clarifying diagnoses.
  12. 8D8B — Disorders affecting autonomic synaptic neurotransmission
  13. 8D8C — Autonomic dysreflexia
  14. 8D8D — Hypoglycaemia unawareness
  15. Paroxysmal autonomic disorders
    It contains 2 clarifying diagnoses.
  16. EE01 — Hypohidrosis
    It contains 5 clarifying diagnoses.
  17. 8D8Y — Other specified disorders of autonomic nervous system
  18. 8D8Z — Disorders of autonomic nervous system, unspecified

The diagnosis is included in 2 other classes.

  • Paroxysmal autonomic disorders
  • Hypohidrosis (EE01)

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