ICD-11 classes
04 Diseases of the immune system
Autoinflammatory disorders

ICD-11 Autoinflammatory disorders

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 5 clarifying diagnoses:

  1. 4A60 — Monogenic autoinflammatory syndromes
    It contains 5 clarifying diagnoses.
  2. 4A61 — SAPHO syndrome
  3. 4A62 — Behçet disease
  4. 4A6Y — Other specified autoinflammatory disorders
  5. 4A6Z — Autoinflammatory disorders, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 1 another class.

  • Schnitzler syndrome (EB03)

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