ICD-11 classes
04 Diseases of the immune system

ICD-11 04 Diseases of the immune system

The diagnosis has no description.

The diagnosis includes nothing.

It excludes 3 items.

  • Complications of pregnancy, childbirth and the puerperium (JA00-JB6Z)
  • Neoplasms (2A00-2F9Z)
  • Developmental anomalies (LA00-LD9Z)

Diagnosis contains 12 clarifying diagnoses:

  1. Primary immunodeficiencies
    It contains 4 clarifying diagnoses.
  2. 4A20 — Acquired immunodeficiencies
    It contains 6 clarifying diagnoses.
  3. Nonorgan specific systemic autoimmune disorders
    It contains 9 clarifying diagnoses.
  4. Autoinflammatory disorders
    It contains 5 clarifying diagnoses.
  5. Allergic or hypersensitivity conditions
    It contains 9 clarifying diagnoses.
  6. Immune system disorders involving white cell lineages
    It contains 15 clarifying diagnoses.
  7. Certain disorders involving the immune system
    It contains 7 clarifying diagnoses.
  8. 4B40 — Diseases of thymus
    It contains 6 clarifying diagnoses.
  9. Organ specific autoimmune disorders
    It contains 1 clarifying diagnosis.
  10. Symptoms, signs or clinical findings of blood, blood-forming organs, or the immune system
    It contains 3 clarifying diagnoses.
  11. 4B4Y — Other specified diseases of the immune system
  12. 4B4Z — Diseases of the immune system, unspecified

The diagnosis is included in 2 other classes.

  • Organ specific autoimmune disorders
  • Symptoms, signs or clinical findings of blood, blood-forming organs, or the immune system (MA00-MA3Y)

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