ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages

ICD-11 Immune system disorders involving white cell lineages

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 15 clarifying diagnoses:

  1. 4B00 — Disorders of neutrophil number
    It contains 3 clarifying diagnoses.
  2. 4B01 — Disorders of neutrophil function
    It contains 4 clarifying diagnoses.
  3. 4B02 — Eosinopenia
    It contains 3 clarifying diagnoses.
  4. 4B03 — Eosinophilia
    It contains 3 clarifying diagnoses.
  5. 4B04 — Disorders with decreased monocyte counts
  6. 4B05 — Disorders with increased monocyte counts
  7. 4B06 — Acquired lymphopenia
  8. 4B07 — Acquired lymphocytosis
    It contains 1 clarifying diagnosis.
  9. 4A01.0 — Immunodeficiencies with predominantly antibody defects
    It contains 8 clarifying diagnoses.
  10. 4A01.1 — Combined immunodeficiencies
    It contains 5 clarifying diagnoses.
  11. 4A00.1 — Defects in the complement system
    It contains 8 clarifying diagnoses.
  12. 4A01.2 — Diseases of immune dysregulation
    It contains 6 clarifying diagnoses.
  13. 4A01.3 — Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
    It contains 5 clarifying diagnoses.
  14. 4B0Y — Other specified immune system disorders involving white cell lineages
  15. 4B0Z — Immune system disorders involving white cell lineages, unspecified

The diagnosis is included in 5 other classes.

  • Immunodeficiencies with predominantly antibody defects (4A01.0)
  • Combined immunodeficiencies (4A01.1)
  • Defects in the complement system (4A00.1)
  • Diseases of immune dysregulation (4A01.2)
  • Other well-defined immunodeficiency syndromes due to defects in adaptive immunity (4A01.3)

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