ICD-11 classes
04 Diseases of the immune system
Certain disorders involving the immune system

ICD-11 Certain disorders involving the immune system

Disorders in which disturbed immune regulation plays an important part but which cannot be more precisely located elsewhere in the classification.

The diagnosis includes nothing.

It excludes 2 items.

  • Failure or rejection of transplanted organs or tissues (NE84)
  • Monoclonal gammopathy of undetermined significance (2A83.0)

Diagnosis contains 7 clarifying diagnoses:

  1. 4B20 — Sarcoidosis
    It contains 8 clarifying diagnoses.
  2. 4B21 — Polyclonal hypergammaglobulinaemia
  3. 4B22 — Cryoglobulinaemia
    It contains 1 clarifying diagnosis.
  4. 4B23 — Immune reconstitution inflammatory syndrome
  5. 4B24 — Graft-versus-host disease
    It contains 4 clarifying diagnoses.
  6. 4A00.14 — Hereditary angioedema
  7. 4B2Y — Other specified disorders involving the immune system

The diagnosis is included in 1 another class.

  • Hereditary angioedema (4A00.14)

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